β-Thalassemia intermedia (β-TI) is a clinical condition of intermediate gravity between thalassemia minor, the asymptomatic carrier, and thalassemia major, the transfusion- dependent, severe anemia. These patients do not require lifelong regular transfusions, although they may need occasional transfusions in certain clinical settings and usually for defined periods of time (surgery, pregnancy, infection). It has a broad clinical spectrum, spanning from asymptomatic mild form with only a slight anaemia (Haemoglobin levels 70-100g/l) to a condition with more severe anaemia revealing itself in the early 2-6 years of life. Since these patients do not usually require routine transfusions, as mentioned above, β-TI has been classified as a non-transfusion-dependent thalassemia [1-3]. These patients require careful attention of the clinician, like thalassemia major, to improve the quality of life [4-7].
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https://juniperpublishers.com/oabtj/OABTJ.MS.ID.555551.php
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